Nokea
Galactosaemia:
- A. Exhibits autosomal recessive inheritance
- B. Is associated with cataracts
- C. Results in a low glucose level
- D. Is due to an inability to convert galactose into glucose
Correct Answer: A
Rationale: Galactosaemia is an autosomal recessive disorder. It is associated with cataracts and results from the inability to convert galactose into glucose.
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Normal Heart
- A. Ventricular septal depolarization occurs from Lt ï‚® Rt
- B. During tachycardia diastolic time reduced than systolic time
Correct Answer: B
Rationale: During tachycardia, diastolic time is significantly reduced compared to systolic time.
Features of severe folate deficiency include:
- A. Steatorrhoea
- B. Glossitis
- C. Leucoerythroblastic picture
- D. Increased total iron binding capacity
Correct Answer: B
Rationale: Glossitis, or inflammation of the tongue, is a common feature of folate deficiency due to its role in cell division and growth.
An 8-month-old infant has a hypercyanotic spell while blood is being drawn. What is the priority nursing action?
- A. Assess for neurologic defects
- B. Place the child in the knee-chest position
- C. Begin cardiopulmonary resuscitation
- D. Prepare family for imminent death
Correct Answer: B
Rationale: The first action is to place the infant in the knee-chest position. Blow-by oxygen may be indicated. Neurologic defects are unlikely. The child should be assessed for airway, breathing, and circulation. Often, calming the child and administering oxygen and morphine can alleviate the hypercyanotic spell.
Polycythaemia:
- A. Is a common cause of jaundice in the newborn
- B. Is significant if haematocrit > 65% on a capillary sample
- C. May cause apnoeas
- D. Exchange transfusion is the treatment of choice in symptomatic cases
Correct Answer: B
Rationale: Polycythaemia is considered significant if the haematocrit exceeds 65% on a capillary sample, as it can lead to hyperviscosity and related complications.
Avascular necrosis of the femoral head is associated with:
- A. Sickle cell trait
- B. Nephrotic syndrome
- C. Cushing's syndrome
- D. Hypothyroidism
Correct Answer: C
Rationale: Cushing's syndrome is associated with avascular necrosis due to steroid use. Sickle cell trait, nephrotic syndrome, and hypothyroidism are not directly linked.