Pediatric HESI Test Bank Related

Review Pediatric HESI Test Bank related questions and content

The nurse is assessing an infant and notes that the infant's urine has a mousy or musty odor. What would the nurse suspect?

  • A. Maple syrup urine disease
  • B. Tyrosinemia
  • C. Phenylketonuria
  • D. Trimethylaminuria
Correct Answer: C

Rationale: The correct answer is C: Phenylketonuria (PKU). PKU is suggested by a mousy or musty odor of the urine, which is caused by the inability to metabolize phenylalanine. Choice A, Maple syrup urine disease, is characterized by a sweet-smelling urine. Choice B, Tyrosinemia, typically presents with cabbage-like odor in the urine. Choice D, Trimethylaminuria, is associated with a fishy odor in the urine, breath, and sweat.