The following conditions are associated with hyperammonaemia:
- A. Reye syndrome
- B. Citrullinaemia
- C. Methylmalonic acidaemia
- D. Homocystinuria
Correct Answer: A
Rationale: Reye syndrome is associated with hyperammonaemia due to liver dysfunction and impaired urea cycle function, leading to ammonia accumulation.
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The initial treatment of choice for a symptomatic patient with isolated pulmonic stenosis is
- A. closed surgical blade valvotomy
- B. open surgical valvotomy
- C. balloon catheter valvuloplasty
- D. Blalock-Taussig shunt
Correct Answer: C
Rationale: Balloon catheter valvuloplasty is less invasive and effective for relieving pulmonic stenosis.
A young female client with seven children is having frequent morning headaches, dizziness, and blurred vision. Her blood pressure (BP) is 168/104 mmHg. The client reports that her husband recently lost his job and she is not sleeping well. After administering a STAT dose of an antihypertensive IV medication, which intervention is most important for the nurse to implement?
- A. Measure urine output hourly to assess for rental perfusion
- B. Request a prescription for pain medication
- C. Use an automated BP machine to monitor for hypotension
- D. Provide a quiet environment with low lighting
Correct Answer: C
Rationale: Monitoring blood pressure is crucial after administering an antihypertensive to ensure the client does not become hypotensive.
Galactosaemia:
- A. Exhibits autosomal recessive inheritance
- B. Is associated with cataracts
- C. Results in a low glucose level
- D. Is due to an inability to convert galactose into glucose
Correct Answer: A
Rationale: Galactosaemia is an autosomal recessive disorder. It is associated with cataracts and results from the inability to convert galactose into glucose.
Increased left ventricular end diastolic volume is seen in:
- A. Mitral regurgitation
- B. Congestive cardiomyopathy
- C. Hypertrophic obstructive cardiomyopathy
- D. Aortic stenosis
Correct Answer: A
Rationale: Mitral regurgitation leads to increased left ventricular end-diastolic volume due to backflow of blood into the left atrium.
Hypothalamic nuclei are responsible for:
- A. Control of hunger
- B. Temperature control
- C. Maintaining osmolarity of extracellular fluid
- D. Secretion of thyrotrophin
Correct Answer: A
Rationale: The hypothalamus plays a key role in regulating hunger through various nuclei and hormonal signals.