Pediatric HESI Test Bank Related

Review Pediatric HESI Test Bank related questions and content

The healthcare provider is assessing an infant and notes that the infant's urine has a mousy or musty odor. What would the healthcare provider suspect?

  • A. Maple syrup urine disease
  • B. Tyrosinemia
  • C. Phenylketonuria
  • D. Trimethylaminuria
Correct Answer: C

Rationale: Phenylketonuria (PKU) is suggested by a mousy or musty odor of the urine, caused by the inability to metabolize phenylalanine. Maple syrup urine disease (Choice A) is characterized by a sweet-smelling urine. Tyrosinemia (Choice B) presents with cabbage-like odor in the urine. Trimethylaminuria (Choice D) results in a fishy odor in the urine, breath, and sweat.